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    • 兔抗GATM多克隆抗體

      規(guī)格:
      價(jià)格:
      • 品牌 : 通蔚生物
      • 目錄號(hào) : TW1285
      • 應(yīng)用 : 僅限于科研使用
      • 貨期 : 現(xiàn)貨
      • 規(guī)格 :100ul/200ul/25ul
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    中文名稱兔抗GATM多克隆抗體


    英文名稱 Anti-GATM rabbit polyclonal antibody


    別       名: glycine amidinotransferase; AT; AGAT; CCDS3


    相關(guān)類別: 一抗

    儲(chǔ)       存 冷凍(-20℃)

    宿       主 Rabbit


    抗       原 GATM


    反應(yīng)種屬 Human, Mouse, Rat


    標(biāo)  記  物 Unconjugate


    克隆類型 rabbit polyclonal


    技術(shù)規(guī)格

    Background:

    This gene encodes a mitochondrial enzyme that belongs to the amidinotransferase family. This enzyme is involved in creatine biosynthesis, whereby it catalyzes the transfer of a guanido group from L-arginine to glycine, resulting in guanidinoacetic acid, the immediate precursor of creatine. Mutations in this gene cause arginine:glycine amidinotransferase deficiency, an inborn error of creatine synthesis characterized by cognitive disability, language impairment, and behavioral disorders.

    Applications:

    ELISA, IHC

    Name of antibody:

    GATM

    Immunogen:

    Fusion protein of human GATM

    Full name:

    glycine amidinotransferase

    Synonyms:

    AT; AGAT; CCDS3

    SwissProt:

    P50440

    ELISA Recommended dilution:

    5000-10000

    IHC positive control:

    Human colorectal cancer

    IHC Recommend dilution:

    50-300



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