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    • 兔抗SGCG多克隆抗體

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      • 品牌 : 通蔚生物
      • 目錄號(hào) : TW21075
      • 應(yīng)用 : 僅供科研使用
      • 貨期 : 現(xiàn)貨
      • 規(guī)格 :25ul
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    中文名稱:  兔抗SGCG多克隆抗體  

    英文名稱: Anti-SGCG rabbit polyclonal antibody

    別    名: A4; MAM; DMDA; SCG3; 35DAG; DAGA4; DMDA1; LGMD2C; SCARMD2; gamma-SG

    相關(guān)類別: 一抗

    抗    原: SGCG

    儲(chǔ)    存 冷凍(-20℃)

    宿    主 Rabbit

    反應(yīng)種屬: Human, Mouse

    標(biāo) 記 物: Unconjugate

    克隆類型: rabbit polyclonal

    技術(shù)規(guī)格

    Background:

    This gene encodes gamma-sarcoglycan, one of several sarcolemmal transmembrane glycoproteins that interact with dystrophin. The dystrophin-glycoprotein complex (DGC) spans the sarcolemma and is comprised of dystrophin, syntrophin, alpha- and beta-dystroglycans and sarcoglycans. The DGC provides a structural link between the subsarcolemmal cytoskeleton and the extracellular matrix of muscle cells. Defects in the encoded protein can lead to early onset autosomal recessive muscular dystrophy, in particular limb-girdle muscular dystrophy, type 2C (LGMD2C).

    Applications:

    ELISA, WB

    Name of antibody:

    SGCG

    Immunogen:

    Synthetic peptide of human SGCG

    Full name:

    sarcoglycan gamma

    Synonyms:

    A4; MAM; DMDA; SCG3; 35DAG; DAGA4; DMDA1; LGMD2C; SCARMD2; gamma-SG

    SwissProt:

    Q13326

    ELISA Recommended dilution:

    5000-10000

    WB Predicted band size:

    32 kDa

    WB Positive control:

    Human heart tissue and Mouse heart tissue lysates

    WB Recommended dilution:

    200-1000



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